Dev retroperitoneal dedifferansiye liposarkom

Abstract

Retroperitoneal sarkomlar; bağ doku, yağ ve kas dokunun mesodermik kök hücrelerinden köken alır ve tüm malign tümörlerin %0,1-%0,2 sini, tüm sarkomların %15 ini oluşturur. Liposarkom en sık görülen tiptir ve bunu leiomyosarkom, malign fibröz histiyositom, fibrosarkom ve diğer undifferensiye sarkomlar takip eder. Kliniğimize sebat eden karın ağrısı ve abdominal distansiyon şikayetleriyle başvuran 53 yaşında erkek hastada yapılan tetkikler neticesinde retroperitoneal bölgede kitle tespit edilmiş ve hasta ameliyata alınmıştır. Ameliyatta, kitle sol böbrek ile beraber eksize edilmiş ve patoloji sonucu dedifferansiye liposarkom olarak raporlanmıştır. Yazıda nadir görülen bir retroperitoneal liposarkom olgusu sunuldu.

Retroperitoneal sarcoma is derived from connective tissue, fat and muscle tissues, and mesodermal stem cells and makes up of 0.1-0.2% of all malignant tumors and 15% of all sarcomas. Liposarcoma is the most common type and is followed by leiomyosarcoma, malignant fibrous histiocytoma, fibrosarcoma and other undifferentiated sarcomas. A 53-year-old man presented to our clinic with persisting complaints of pain and abdominal distention. A mass was detected at the retroperitoneal region after radiological examination and the patient was taken to surgery. During the operation, the mass was totally excised with the left kidney. The mass was sent for pathological examination and was reported as dedifferentiated liposarcoma. In this report, a rare case of retroperitoneal liposarcoma is presented.